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y acumulacin intracelular de amonio en forma similar a lo que ocurre en el dficit de la enzima CPS I
In a study by Topcu-Tarladacalisir et al

doi: 10.1126/science.aan5931 103 ZhengRWangGPangZRanNGuYGuanXet al

Zloenie isten voda, L-Carnitin, kyselina citrnov, arma, kyselina sorbov, benzoan sodn, sladidlo- acesulfam K, sukralza
