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Description
349 Similarly, mutations in valosin-containing protein (VCP), a multifunctional AAA-ATPase essential for extracting ubiquitinated proteins from cellular structures and directing them toward degradation, cause multisystem proteinopathies that include ALS, FTD, and inclusion body myopathy
PMID 11881712

Finally, with regard to excretion, BBR is predominantly eliminated via urine and bile in its metabolized forms

In experimental systems, TB-500 is used to investigate actin dynamics, endothelial cell behavior, cellular migration, and extracellular matrix remodeling processes
