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Importantly, clinical studies typically have indiscriminately tested interventions and have rarely utilised biomarkers or clinical symptoms to identify treatment responders, so the clinical indications are in some cases based on the authors opinion regarding the rationalisation of different management options

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& Lee-Visser, J

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Carnitine and/or acetylcarnitine deficiency as a cause of higher levels of ammonia

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[9] How quickly should I notice an effect

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