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Description
En los complementos es preferible utilizar las sales de L-carnitina fumarato o tartrato y acetil L-carnitina por su estabilidad, mejorando significativamente el nivel plasmtico de L-carnitina

SLC22A5 mutations impair OCTN2 function, causing primary carnitine deficiency (PCD) ( Beyond genetic determinants, OCTN2 expression and function undergo significant physiological and pharmacological regulation

Transporta cidos graxos atravs das membranas celulares at s mitocndrias , onde ocorre a beta-oxidao (queima) para serem transformados em energia

showed the effectiveness of hemodialysis in the clearance of ammonia in a patient with OTC deficiency
